Cystic lymphangioma is a rare tumour (6 % of benign tumours in childre
n), frequently situated in the cervical or axillary region and excepti
onally intraabdominal. It arises due to a congenital defect in the con
nection of the primary lymphatic channels with the central collecting
system. It presents clinically either in the form of a pseudo-appendix
or pseudo-ascites syndrome or in the form of an abdominal tumour with
or without compression of adjacent structures. It can now be easily d
iagnosed by ultrasonography. Treatment is well defined and consists of
surgical resection of the isolated lymphangioma or associated with th
e adjacent intestine, depending on the site of the tumour. It has a go
od prognosis.