A 64-year-old man affected by acute monoblastic leukemia developed a c
utis verticis gyrata during the terminal phase of hemopathy. The assoc
iation between these two diseases is rare. The classification of cutis
verticis gyrata in primary essential, primary non-essential and secon
dary forms is reviewed. Performing a skin biopsy is necessary in the d
iagnostic approach to patients with cutis verticis gyrata.