WILMS-TUMOR IN THE LI-FRAUMENI CANCER FAMILY SYNDROME

Authors
HARTLEY AL BIRCH JM TRICKER K WALLACE SA KELSEY AM HARRIS M JONES PHM
Citation
Al. Hartley et al., WILMS-TUMOR IN THE LI-FRAUMENI CANCER FAMILY SYNDROME, Cancer genetics and cytogenetics, 67(2), 1993, pp. 133-135
Citations number
19
Categorie Soggetti
Oncology,"Genetics & Heredity
Journal title
Cancer genetics and cytogenetics → ACNP
ISSN journal
01654608
Volume
67
Issue
2
Year of publication
1993
Pages
133 - 135
Database
ISI
SICI code
0165-4608(1993)67:2<133:WITLCF>2.0.ZU;2-R
Abstract
Scrutiny of the family pedigrees of a population-based series of 176 c hildren diagnosed with Wilms' tumor between 1954 and 1990, along with a review of the literature on the Li-Fraumeni cancer family syndrome, indicate that Wilms' tumor may be an uncommon component of the syndrom e and that a small proportion of children with Wilms' tumor may be mem bers of Li-Fraumeni syndrome (LFS) families.