CORNEAL ABNORMALITIES ASSOCIATED WITH INCONTINENTIA PIGMENTI

PURPOSE: To report corneal abnormalities associated with incontinentia pigmenti. CASE REPORTS: Two girls, aged 2 1/2 and 5 years, with incon tinentia pigmenti from one family underwent a complete ophthalmic exam ination. RESULTS: We found vortex (whorl-like) epithelial keratitis ch aracterized by epithelial microcysts that stained with fluorescein and midstromal radial mild haziness in daughters of a family with inconti nentia pigmenti. CONCLUSION: Incontinentia pigmenti should be included in the differential diagnosis of children with keratitis, particularl y if there is evidence of characteristic dermatologic or other systemi c manifestations.