CEREBRAL RETROFLEXION IN HOLOPROSENCEPHALY DEVELOPED FOLLOWING VENTRICULO-PERITONEAL SHUNTING - A CASE-REPORT

Retroflexion of the hypoplastic fused cerebrum is a rare condition in holoprosencephaly. We describe a new case of this entity in a 7-year-o ld boy with alobar holoprosencephaly who developed retroflexion of the holosphere 7 years after a ventriculo-peritoneal shunt was placed. Th e radiological findings revealed retroflexion of the cerebrum anchored to the cranial vault between the precerebral space and the dorsal sac , which were open to each other. In patients with holoprosencephaly, t he possibility of retroflexion of the holosphere should be considered after placement of a ventriculo-peritoneal shunt for associated hydroc ephalus.