COMPROMISE OF THE SPINAL-CANAL IN PROTEUS SYNDROME

Authors
SKOVBY F GRAHAM JM SONNEHOLM S COHEN MM
Citation
F. Skovby et al., COMPROMISE OF THE SPINAL-CANAL IN PROTEUS SYNDROME, American journal of medical genetics, 47(5), 1993, pp. 656-659
Citations number
7
Categorie Soggetti
Genetics & Heredity
Journal title
American journal of medical genetics → ACNP
ISSN journal
01487299
Volume
47
Issue
5
Year of publication
1993
Pages
656 - 659
Database
ISI
SICI code
0148-7299(1993)47:5<656:COTSIP>2.0.ZU;2-W
Abstract
We report on 2 children with spinal stenosis and neurologic sequelae. They illustrate the 2 ways in which spinal compromise may develop in P roteus syndrome vertebral anomalies or tumor infiltration. In one pati ent, spinal stenosis resulted from an angular kyphoscoliosis. In the o ther, cord compression resulted from infiltration of a paraspinal, int rathoracic angiolipoma. (C) 1993 Wiley-Liss, Inc.