TURNER SYNDROME AND OCCLUSION OF THE INTERNAL CAROTID-ARTERY

A 2-year-old girl with Turner syndrome was admitted with left hemipleg ia and left facial palsy. Serial cranial computed tomographic scan dem onstrated multiple cerebral infarctions in the right putamen and right medial cortical areas. Single photon emission computed tomographic sc an revealed hypoperfusion from the right frontal to the right temporal area. Right carotid angiography showed narrowing and occlusion of the right internal carotid artery at the sphenoidal portion. Collateral c irculation was not detected between the external and internal carotid arteries. Left carotid angiography revealed that the left anterior art ery was narrow, and that the left internal carotid artery provided blo od to the right internal carotid artery through the anterior communica ting artery. These findings suggested that the cerebrovascular abnorma lity might be due to congenital hypoplasia of arteries in this patient . The unusual combination of cerebral infarction and Turner syndrome w as reported.