Objective: This study aimed to review the management of cerebrospinal fluid
(CSF) fistulae in the setting of developmental inner ear deformity,
Study Design: The study design was a case review close examination of preop
erative radiology, and corresponding intraoperative images.
Technique: A definitive method of CSF fistula closure is described using pr
eviously known techniques used commonly in skull base surgery.
Conclusions: The use of a multiple-level, reinforced wound closure techniqu
e is necessary to definitively close CSF fistulae in extreme inner ear defo
rmity and to prevent further episodes of CSF leak and meningitis.