A case study of single ventricle (cor triloculare biatriatum)

Univentricular hearts represent rare complex cardial malformations. We repo rt a case of a 34-year old male with single ventricle, two atria, tricuspid atresia,large atrial septal defect, complete transposition and pulmonary v alvar stenosis. There were no signs of chronic pulmonary hypertension. Inte nsive clinical analysis of the cardiac malformation was first performed at the age of five yea rs. Conclusion was that the patient would have no benef it from operation. The patient had nearly normal live conditions with a pro fession, family and some sportive activities like squash. He died of sudden cardiac death. The malformation was examined by sequential segmental analy sis and in comparison with the embryonic development. Special features are emphasized. Clinical picture, prognosis and therapy are reported from liter ature. During the last years development of cardiac surgery achieved good r esults. Special morphologic constellations, as in our case, may be the reas on that conservative therapy can be sufficient for prolonged survival with good quality of life.