Residual deformity in congenital radial club hands after previous centralisation of the wrist - Ulnar lengthening and correction by the Ilizarov method

We used the Ilizarov method in seven patients with severe congenital radial club hands who had had previous wrist surgery, to correct residual shorten ing and bowing of the ulna together with recurrent wrist deformity. The mean age at operation was 6.5 years, The mean ulnar shortening was 5.3 cm and the mean angular deformity 42 degrees. The mean length gained was 51% of the original ulna, The mean healing index was 46.9 days (29.8 to 64.0). The ratio of the length of the lengthened ul na to the normal side improved on average from 64% to 95%, The angular defo rmity was initially completely corrected in six out of seven patients. The length ratio, however, decreased to 83% at the final follow-up, In four pat ients, the angular deformity partially recurred. We recommend correction of congenital radial club hand by staged procedures . The first is centralisation and stabilisation of the wrist and the second lengthening of the ulna and correction of the angular deformity using the Ilizarov method.