Childhood vulval lichen sclerosus is a patient with ectodermal dysplasia and uncombable hair

An 11-year-old girl was diagnosed as having ectodermal dysplasia, with abno rmalities of her nails, teeth, and hair noted From infancy. Her hair was un ruly and investigations confirmed the changes seen in "cheveux incoiffables "-the uncombable hair syndrome. She also had atopy requiring treatment to c ontrol asthma and eczema. When she was 8 years old she developed vulval lic hen sclerosus, which was controlled easily with early treatment. The coexis tence of these conditions is discussed.