This case describes a man with progressive refractory epilepsy whose death
was witnessed during a seizure. Initial brain imaging was normal, but follo
wing prolonged episodes of non-convulsive status epilepticus, progressive r
ight-sided temporal atrophy developed over a period of two years. The clini
cal picture and postmortem examination were consistent with the diagnosis o
f Rasmussen's encephalitis, a rare condition with a bleak prognosis.