J. Ikeda et al., Pineoblastoma presenting in familial adenomatous polyposis (FAP): random association, FAP variant or Turcot syndrome?, BR J NEUROS, 12(6), 1998, pp. 576-578
Brain tumours which arise in combination with adenomatous polyposis are usu
ally astrocytic rumours or medulloblastomas. An adult women with a pineobla
stoma associated with familial adenomatous polyposis is presented. In regar
d to the neuro-epithelial origin of this tumour we propose that it should b
e included in the second category of brain tumour polyposis syndrome.