Peeling skin syndrome with hair changes

A 13-year-old boy with typical peeling skin syndrome (PSS) is described. Th e clinical picture corresponded to the inflammatory variant of PSS (type B) . In addition, the patient had gross and microscopic hair anomalies such as trichorrhexis invaginata-like changes, irregular hair shaft torsions and m oniliform hair shaft diameter reductions. The observed dysmorphic hair chan ges are discussed and interpreted as being an integral component of the der matosis in this case. To the best of our knowledge, such hair anomalies hav e not yet been described in PSS.