Bilateral and multicystic major salivary gland disease: a rare presentation of primary Sjogren's syndrome

We present a case of a 15-year-old girl with bilateral parotid and sub-mand ibular salivary gland enlargement as the sole presentation of primary Sjogr en's syndrome. The clinical, radiological, immunological and pathological f eatures have been discussed. The relevant literature has been reviewed. To our knowledge this is the only reported case of Sjogren's syndrome presenti ng as multicystic disease with bilateral major salivary gland involvement.