Intracaval extension of a recurrent low-grade endometrial stromal sarcoma

We report the case of a patient undergoing successful removal of an intraca val extension of a recurrent low-grade endometrial stromal sarcoma sixteen years after complete surgical resection. Low-grade endometrial stromal sarc oma is rare uterine neoplasm with a excellent 5-year survival but with high incidence of relapse after a very long time. The tumour has a tendency for lymphatic and venous extension. Intracaval extension is an exceptional ind ication to perform caval surgery in the treatment of malignant neoplasm.