Successful heart transplantation in a patient with Ivemark syndrome combined with situs inversus, single atrium and ventricle after total cavo-pulmonary connection

Heart transplantation represents a valuable therapeutical option for patien ts with congenital heart disease and end-stage heart failure. We report the case of a young adult patient with a situs inversus and additional complex congenital malformations of the heart who underwent several prior palliati ve interventions, a biventricular repair being impossible. Orthotopic cardi ac transplantation with several technical modifications was performed succe ssfully at the age of 19 years. (C) 1998 Elsevier Science B.V. All rights r eserved.