RHABDOMYOSARCOMA OF THE BILIARY TREE

Rhabdomyosarcoma (RMS) of the biliary tree is a rare tumor in children that has a very poor prognosis. Preoperatively, it is often mistaken for a choledochal cyst. We report a case of RMS of the biliary tree in a 4-year-old girl who presented with abdominal pain and obstructive j aundice. The RMS was diagnosed at laparotomy; excision was not possibl e due to its size and localization. Chemotherapy achieved complete reg ression of the tumor observed at second-look surgery. Preoperative che motherapy can now avoid mutilating surgical procedures and improve sur vival.