Chondroid syringoma is a rare subcutaneous tumor that mainly affects the fa
ce and the neck. The authors present an occurrence in the orbit, which they
believe to be the first reported at that site. Computed tomography and mag
netic resonance imaging suggested that the tumor had invaded the globe, but
at surgery the mass was well circumscribed and did not invade or adhere to
other structures. The tumor was resected easily under general anesthesia.
Epithelial cells of characteristic appearance within a chondroid matrix wer
e demonstrated histologically. No recurrence has been evident in more than
1 year of follow-up. Most chondroid syringomas are benign, but because seve
ral cases have exhibited malignant behavior, periodic observation following
complete resection is required.