We retrospectively evaluated maternal and fetal outcomes in a series of wom
en with von Hippel-Lindau disease. Data resulted from 56 pregnancies in 30
women. Symptoms related to von Hippel-Lindau disease occurred in 3 of 56 pr
egnancies, in this unselected group of patients with von Hippel-Lindau dise
ase, most pregnancies had a favorable outcome with a 96.4% survival rate fo
r fetuses and a 5.4 % von Hippel-Lindau-specific morbidity rate in the moth
ers.