COEXISTENCE OF A GRAFT WITH THE PRESERVED NATIVE LIVER IN AUXILIARY PARTIAL ORTHOTOPIC LIVER-TRANSPLANTATION FROM A LIVING DONOR FOR ORNITHINE TRANSCARBAMYLASE DEFICIENCY

Background. Auxiliary partial orthotopic liver transplantation (APOLT) has recently been performed in patients with noncirrhotic metabolic l iver diseases. However, long-term outcomes for the preserved native Li ver and the transplanted liver graft have not been clearly established yet. Methods. The recipient was a 36-month-old girl with ornithine tr anscarbamylase deficiency. She underwent APOLT, using her father's lef t lateral segment. Results. Liver function was normalized soon after A POLT and the patient was able to ingest a normal diet without medicati on Coexistence of the well-functioning native liver and graft was demo nstrated in a computed tomography scan, Doppler ultrasonography, scint igraphy, and histological examination, during a relatively long-term f ollow-up period. Conclusions. APOLT seems to be most useful far the tr eatment of noncirrhotic metabolic liver diseases.