Rectal ectasia may be associated with anorectal anomalies, If not reco
gnized at the time of surgical reconstruction it may lead to megarecto
sigmoid, resulting in severe constipation and overflow incontinence po
stoperatively, The authors treated four patients presenting with this
condition, One patient born with a low anorectal anomaly and two with
high anorectal anomalies experienced intractable constipation caused b
y megarectum despite otherwise adequate primary reconstructive procedu
res, A fourth patient had rectal stenosis in association with megarect
osigmoid, The ectatic megarectum had to be resected in all the patient
s to achieve normal bowel actions. The authors feel that resection or
tailoring of the ectatic segment should be an integral part of the pri
mary reconstructive procedure. Copyright (C) 1997 by W.B. Saunders Com
pany.