Pheochromocytoma and von Recklinghausen neurofibromatosis presenting with a crisis during the puerperal period. Report of one case

lPheochromocytoma is observed with higher frequency?, in patients with coil Recklinghausen neurofibromatosis. We report a 36 years old female with von Recklinghausen neurofibromatosis who developed mild hypertension during: t he fourth,month of pregnancy. A cesarean section was performed at 37 weeks of pregnancy. Thereafter; the patient presented severe hypertensive and hyp otensive Crises sinus tachycardia and fever:No evidences of an infections d isease were found. Abdominal ultrasound examination showed a right adrenal mass of 7 x 5 cm. High levels Of urinary cathecolamines confirmed the diagn osis of pheochromocytoma. After, three weeks of prazosin therapy, the patie nt wets operated. During the surgical procedure, an encapsulated pheochromo cytoma was found and excised A right renal atrophy and renal artery thrombo sis were also found and a nephectomy was done. Postoperative evolution was uneventful and the patient remains with normal blood pressure levels six mo nths after the operation.