Primary aortoenteric fistulae (AEFs) are extremely rare vascular entities,
with fewer than 250 cases reported in the world medical literature as of 19
96. incidence is less than 1 per cent, with a mortality ranging from 33 to
85 per cent. Atherosclerosis remains the most common etiology, accounting f
or more than two-thirds of the cases reported. Other etiologies include car
cinoma, ulcers, gallstones, diverticulitis, appendicitis, and foreign bodie
s. Early diagnosis is crucial for survival and mandates recognition of the
typical "herald bleed." Additional findings on initial presentation frequen
tly include flank pain, abdominal pain, hematemesis, melena, and an abdomin
al mass. More than 80 per cent of primary AEFs involve the duodenum, with t
he overwhelming majority located in the third or fourth portion. Successful
management of primary AEF requires a high index of suspicion for diagnosis
and prompt surgical intervention for survival.