Lacrimal gland choristoma of the iris

Intraocular lacrimal gland tissue is an extremely rare choristoma. A newbor n girl was seen with a fleshy, vascular tumor arising from the peripheral i ris and the anterior chamber angle, The tumor was treated with topical ster oids on suspicion of a juvenile xanthogranuloma; Later, it grew slightly an d a secondary glaucoma developed, Histopathological examination of the rese cted tumor showed lacrimal gland tissue in the iris. Twelve cases of intrao cular lacrimal gland tissue have been reported in the literature.