The role of the glutamate receptor GluR3 in Rasmussen's encephalitis is act
ively under investigation. Autoimmune processes with this receptor as thr t
arget are currently theorized. We provide an additional case of pathologica
lly proved Rasmussen's encephalitis (with concomitant cortical dysplasia) i
n the presence of antibodies against the GluR3 receptor.