Splenic involvement is rare in patients with hydatid disease even in e
ndemic countries. The spleen is the third most commonly involved organ
after the liver and the lung. In our series splenic echinococcosis re
presents 5.8% of abdominal hydatid disease. During the last 22 years,
14 patients were operated on for splenic hydatid cysts in our departme
nt. In 10 patients the spleen was the only location of hydatid disease
; in 2 patients there was concomitant liver hydatid disease; one patie
nt had disseminated intraabdominal disease; and one patient bad a coex
isting hydatid cyst in the quadriceps femoris muscle. Plain abdominal
films, ultrasonography, and computed tomography scans were most useful
for establishing the diagnosis. All patients underwent splenectomy al
one or combined with management of cysts at other sites, except for tw
o patients who underwent omentoplasty and one patient who underwent ex
ternal drainage. One patient died during the early postoperative perio
d (mortality rate 7%), and three patients had minor complications. Spl
enic hydatid disease should be included in the differential diagnosis
when a splenic cyst is identified, especially in patients with a histo
ry of hydatid disease. Surgery remains the treatment of choice to avoi
d serious complications.