Dieulafoy's lesion is an abnormal submucosal artery in the gastrointestinal
tract characterized by massive gastrointestinal bleeding. We describe a pa
tient who developed Dieulafoy's lesion or the esophagus in the course of is
olated pulmonary Takayasu's arteritis. Angiographic findings indicated a re
lationship between pulmonary arterial involvement of Takayasu's disease and
Dieulafoy's lesion of the esophagus. This observation represents the first
report of the association between Takayasu's arteritis and Dieulafoy's les
ion of the esophagus.