We report a case of portal hypertension and neutrocytic ascites in a 52 yea
r old man with POEMS syndrome. POEMS syndrome is an association of polyneur
opathy, organomegaly, endocrinopathy, monoclonal gammapathy and skin change
s. Portal hypertension is rare in POEMS syndrome and this is the first time
that culture negative neutrocytic ascites has been described with this syn
drome.