Benign osteonecrosis (EON) of the external ear canal (EEC), also terme
d as focal or circumscribed necrotizing lesion, is an infrequent pheno
menon with distinctive features and of an obscure origin, Five patient
s with BON of the EEC presented with aggressiveness and extension of v
arying degree including involvement of the middle ear, It seems that t
he disease might have a self limited course (two patients) though, at
times, extensive measures including hyperbarric oxygen therapy (one pa
tient) should be applied.