The co-existence of horseshoe kidney (HSK) and abdominal aortic aneury
sm (AAA) is rare and demands a special diagnostic workup and a meticul
ous surgical procedure. Ten patients with HSK associated with AAA are
reported. All underwent aortic replacement with successful preservatio
n of multiple renal arteries. One patient died at the 7th postoperativ
e day from myocardial infarction. HSK does not represent a contraindic
ation for aortic repair. Angiography for identification of aberrant re
nal arteries and classification into three types for surgical manageme
nt is mandatory. In type I and II we recommend a standard midline tran
speritoneal approach. Only in type III does a thoraco-abdominal approa
ch seem favourable. The aortic reconstruction should be performed with
tube grafts, if possible. Aberrant renal arteries are reattached dire
ctly to the prosthesis. Dissection of renal isthmus should be avoided.
Temporary cold renal perfusion is indicated to extend the ischemic to
lerance time. As repair of a ruptured AAA in patients with HSK may be
quite difficult and time consuming, we recommend more liberal indicati
ons for aneurysm surgery in patients with HSK.