Pseudomyxoma retroperitonei with spontaneous skin fistula

We describe the imaging features in a patient with pseudomyxoma; retroperit onei arising from a mucinous carcinoma of the appendix with spontaneous dev elopment of a skin fistula: The thick wall and septa characteristic of pseu domyxoma were best demonstrated on gadolinium-enhanced: magnetic resonance imaging. This patient illustrates (a) the potential of pseudomyxoma to caus e skin fistula and (b) the possibility that this' intraabdominal process ca n first present as a dermatologic complication.