Pancreatic inflammatory tumour: a rare entity in childhood

Citation
Kr. Shankar et al., Pancreatic inflammatory tumour: a rare entity in childhood, J ROY COL S, 43(6), 1998, pp. 422-423
Citations number
10
Categorie Soggetti
Surgery
Journal title
JOURNAL OF THE ROYAL COLLEGE OF SURGEONS OF EDINBURGH
ISSN journal
00358835 → ACNP
Volume
43
Issue
6
Year of publication
1998
Pages
422 - 423
Database
ISI
SICI code
0035-8835(199812)43:6<422:PITARE>2.0.ZU;2-Q
Abstract
Pancreatic rumours are rare childhood neoplasms. Inflammatory myofibrohisti ocytic tumours (IMTs) represent an uncommon but distinct pathological subgr oup that creates diagnostic and therapeutic dilemmas. We report a case of I MT arising from the body and tail of the pancreas in an 8-year-old girl pre senting with a mass and abdominal pain. A locally aggressive tumour with no evidence of distant metastasis was encountered at laparotomy and resected. Pathologically, the tumour revealed a mixed inflammatory cell infiltrate w ith myofibrohistiocytic proliferation. These features can resemble a sarcom a. A review of the Literature is provided which emphasises the clinical fea tures, pathological findings, and management strategies for these unusual r umours. Complete surgical excision, aided by radiological surveillance, app ears to offer the best guidelines for definitive management.