Pancreatic rumours are rare childhood neoplasms. Inflammatory myofibrohisti
ocytic tumours (IMTs) represent an uncommon but distinct pathological subgr
oup that creates diagnostic and therapeutic dilemmas. We report a case of I
MT arising from the body and tail of the pancreas in an 8-year-old girl pre
senting with a mass and abdominal pain. A locally aggressive tumour with no
evidence of distant metastasis was encountered at laparotomy and resected.
Pathologically, the tumour revealed a mixed inflammatory cell infiltrate w
ith myofibrohistiocytic proliferation. These features can resemble a sarcom
a. A review of the Literature is provided which emphasises the clinical fea
tures, pathological findings, and management strategies for these unusual r
umours. Complete surgical excision, aided by radiological surveillance, app
ears to offer the best guidelines for definitive management.