Granulomatous cheilitis and Crohn's disease are disorders of unknown etiolo
gy. There are case reports describing their coincidence and pointing out th
e necessity of ruling out systemic disorders once the diagnosis of granulom
atous cheilitis is made. However, such reports are few and the causal assoc
iation of both diseases is controversial in the literature. We report the y
oungest patient so far, a 3-year-old boy, who had granulomatous cheilitis a
nd Crohn's disease simultaneously. This coincidence so early in life strong
ly suggests that both represent manifestations of the same disease.