Gf. Grekas et al., COMPLETE HEART-BLOCK IN THE SETTING OF MITOCHONDRIAL CYTOPATHY - IMPLANTATION OF A PERMANENT PACEMAKER IN A 6-YEAR-OLD BOY, PACE, 20(4), 1997, pp. 995-996
The case of a 6-year-old boy with cytochrome oxidase (complex IV) defi
ciency and complete heart bloc, treated with permanent pacemaker impla
ntation, is reported.