We report an 80-year-old woman with a bilateral mutilating acro-osteolysis
of the fingers progressing over a period of 3 years. As the patient refused
nerve or muscle biopsies, our diagnosis of acropathia ulcero-mutilans acqu
isita or Bureau-Barriere syndrome, characterized by osteolysis, remains hyp
othetical. Sporadic sensory mutilating acropathy of the upper limbs is rare
, and we discuss the differential diagnosis.