Congenital varicella syndrome: cranial MRI in a long-term survivor

Congenital varicella syndrome is a rare disorder which follows maternal inf ection in the first or early second trimester, The syndrome comprises a num ber of malformations including microcephaly, cortical destruction and limb hypoplasia, We describe a case where there has been long-term survival foll owing second trimester maternal infection. The clinical findings, including the characteristic lower limb hypoplasia, are documented, as are the appea rances on cranial MRI indicating an encephaloclastic porencephaly.