Extra-abdominal fibromatosis (desmoid tumor) arising in the infratemporal fossa: A case report

Aggressive fibromatosis (or desmoid tumor) refers to a histologically benig n but locally aggressive lesion arising from musculoaponeurotic structures in various anatomic sites. Extra-abdominal desmoids represent about one thi rd of all desmoid tumors; of these only about 11 to 15% arise in the head a nd neck, Desmoid tumors arising in the infratemporal fossa are exceedingly rare; to our knowledge only one such tumor has been reported in the literat ure. We present a desmoid tumor arising in the infratemporal fossa with int racranial extension in a twenty-seven year old male, and review the literat ure on this rare condition.