Giant cell tumor of the sphenoid bone

Objective and Importance: Giant cell tumor of the sphenoid bone is extremel y unusual. This tumor is usually located in long bones and is rarely locate d in the cranial vault. It must be differentiated from reparative granuloma and the Brown tumor of hyper parathyroidism. This case report is only the second involving a patient in the first decade . Clinical Presentation: A 9-year-old girl presented with cephalgia and diplo pia, Radiographic imaging revealed an erosive mass in the clivus. Intervention: The patient underwent an extended transphenoidal resection of the clivus; This was followed with 57.6 CGE in 32 fractionated doses. Conclusion: At 1 year follow-up, the tumor remains stable. Based on anecdot al evidence, at tempted resection with adjuvant radiation therapy allows fo r long-term survival in these patients.