Malignant chondroid syringoma, a very rare tumour, presenting with mul
tiple pulmonary metastases in a 50 year old woman is described. Initia
l diagnostic confusion with pulmonary hamartoma occurred due to histop
athological similarities. However, re-examination of a skin biopsy spe
cimen taken 17 years previously from a hand lesion yielded the necessa
ry information to identify the pulmonary lesions definitively as metas
tases from the original skin lesion. The features of this very rare in
dolent tumour are described.