4TH VENTRICULAR EPENDYMOMA IN A CHILD WITH DUANE RETRACTION SYNDROME

A child with unilateral Duane retraction syndrome developed signs and symptoms of increased intracranial pressure at 3 1/2 years of age. Neu roimaging disclosed a fourth ventricular ependymoma compressing but no t invading the floor of the fourth ventricle. The coexistence of Duane syndrome and fourth ventricular ependymoma in a young child raises th e possibility that both conditions could have resulted from a mutation al event or focus of cellular disorganization (i.e. field defect) loca lized to the dorsal pens.