RESTRICTIVE CARDIOMYOPATHY DUE TO PRIMARY AMYLOIDOSIS AL

Citation
Y. Ruckert et al., RESTRICTIVE CARDIOMYOPATHY DUE TO PRIMARY AMYLOIDOSIS AL, Zeitschrift fur Kardiologie, 86(10), 1997, pp. 812-817
Citations number
15
Categorie Soggetti
Cardiac & Cardiovascular System
Journal title
ISSN journal
03005860
Volume
86
Issue
10
Year of publication
1997
Pages
812 - 817
Database
ISI
SICI code
0300-5860(1997)86:10<812:RCDTPA>2.0.ZU;2-H
Abstract
In a 71-year-old woman with macroglossia and heart failure, a monoclon al protein (kappa-light chains) was found in the serum. Congestive hea rt failure was diagnosed on the basis of heart catheterization and ech ocardiography. The tongue biopsy showed numerous amyloid fibrils, and plasmacytosis was present in the bone marrow. AII these findings indic ated a restrictive cardiomyopathy as part of a primary systemic amyloi dosis.