One of the most frequent causes of sensorineural hearing loss in child
hood is damage to outer hair cells of the cochlea. The presence of oto
acoustic emissions, generated by outer hair cells, provides evidence f
or normal hearing. This finding, however, may give rise to false reass
urance, because even severe hearing loss, localized behind the cochlea
, can be associated with normal otoacoustic emissions. The coexistence
of otoacoustic emissions and hearing loss calls for the prompt exclus
ion of neurological disease.