Pilomatricoma is a skin appendage tumor that frequently involves the s
kin of the head, neck, and upper extremities in young children. In thi
s prospective study, we present and discuss the characteristics of our
patients with pilomatricoma. During the years 1984 to 1994, 15 childr
en (9 girls and 6 boys) with pilomatricoma were admitted to our servic
e. Their ages ranged from 3 to 13 years (mean age 9 years). All of the
lesions of these patients were excised totally. On histopathologic ex
amination, calcification was found in all of the specimens, No invasio
n or malignancy was observed by light microscopy, All patients have be
en followed up periodically by the same surgeons. Interestingly, we fo
und two familial occurrences and four multiple occurrences. Although o
ur series was too small for accurate statistical evaluation, multiple
and familial occurrences of pilomatricoma (26.7% and 13.3%, respective
ly) were higher than in previously reported series.