COCHLEAR IMPLANTATION IN PATIENTS WITH COGANS-SYNDROME - A REVIEW OF 4 CASES

Cogan's syndrome is a rare disorder that is characterized by a rapid o nset of bilateral severe sensorineural hearing loss associated with ve rtigo and tinnitus, ocular involvement (most commonly an interstitial keratitis) and variable systemic symptoms. We review our experience wi th four cases treated in our department. We describe their symptoms, t he evolution of their disease, the diagnosis, and the radiological inv estigations with computed tomography and/or magnetic resonance imaging . When medical treatment with corticosteroids failed and no benefit co uld be obtained with hearing aids at each patient's end stage, all pat ients received a cochlear implant with excellent results. The consider ations for implantation in these patients are discussed.