Cementifying fibromas are rare fibro-osseous tumors that arise from th
e periodontal ligament. These tumors are usually small, asymptomatic l
esions noted on routine dental radiography, but they can develop into
aggressive, expansile masses. The authors report the case of a 12-year
-old boy with a tumor involving the maxillary, ethmoid, and frontal si
nuses that extended to the right orbit, causing proptosis and disfigur
ement of the right side of his face. Removal of the tumor with facial
reconstruction resulted in significant improvement of vision, despite
long-standing disc edema and tension on the optic nerve. On histopatho
logic examination the lesion was found to be a cementifying fibroma.