PULMONARY CAPILLARY HEMANGIOMATOSIS - RADIOGRAPHIC APPEARANCE

Pulmonary capillary hemangiomatosis is a rare disorder that is charact erized pathologically by formation of capillaries along alveolar walls that may ultimately invade the pulmonary parenchyma and pulmonary art eries. The clinic presentation overlaps that of primary pulmonary hype rtension, but the natural history of pulmonary capillary hemangiomatos is is one of rapid deterioration. The typical radiographic appearance is a diffuse bilateral reticulonodular pattern associated with enlarge d central pulmonary arteries.