Patent urachus results when there is a persistence of an allantois rem
nant which normally undergoes atresia during embryological development
. It can lead to an abdominal wall defect similar in appearance on ult
rasound to an omphalocele. A 34-year-old primigravida presented at 19
weeks' gestation for evaluation of a cystic mass arising at the umbili
cal cord insertion. The initial impression of the referring physician
was an omphalocele. The mass arose from the abdominal wall and the umb
ilical cord inserted into the membranous covering of the mass, which a
ppeared to be fluid-filled and separate from but contiguous with the u
rinary bladder. Serial sonography followed the progression of the abdo
minal wall mass. At term, the patient underwent primary Cesarean secti
on with delivery of a 4494-g male infant. The infant underwent repair
and closure of the patent urachus and plastic reconstruction of the ab
dominal wall. When the urachus remains patent, it can lead to a urinar
y fistula which mimics the ultrasound appearance of an omphalocele. Ho
wever, patent urachus is associated with a much lower rate of abnormal
ities than omphalocele, yielding a better fetal prognosis.