Intraventricular craniopharyngiomas are rare rumours. They are wholly
within the third ventricle and can be distinguished from suprasellar l
esions which extend into the third ventricle by the presence of an int
act floor of the third ventricle. They are attached to the wall of the
third ventricle to a variable extent, most commonly in the region of
the tuber cinereum. The long-term follow-up on six cases treated by on
e of the authors is presented. Headache and visual disturbance were th
e most common presenting features but, unlike the more common suprasel
lar lesions, symptomatic endocrine disturbances were not a common pres
enting feature. Total surgical removal can cause hypothalamic damage a
nd the resulting morbidity can be serious and sometimes life-threateni
ng. Subtotal removal followed by radiotherapy is probably the treatmen
t of choice for these lesions.