M. Ruscazio et al., INTERRUPTED INFERIOR VENA-CAVA IN ASPLENIA SYNDROME AND A REVIEW OF THE HEREDITARY PATTERNS OF VISCERAL SITUS ABNORMALITIES, The American journal of cardiology, 81(1), 1998, pp. 111
We present the clinical and postmortem findings of the first photograp
hically documented case of asplenia and interrupted inferior vena cava
and the anatomic findings of 5 previously reported cases. A brief rev
iew of the various hereditary patterns of visceral situs abnormalities
suggests that, at least in some cases, the asplenia and polysplenia s
yndromes are etiologically and pathogenetically interrelated.